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Child's Nervous System
Published in: Child's Nervous System 10/2019

01-10-2019 | Syringomyelia | Special Annual Issue

Defining, diagnosing, clarifying, and classifying the Chiari I malformations

Authors: Stephen Bordes, Skyler Jenkins, R. Shane Tubbs

Published in: Child's Nervous System | Issue 10/2019

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Abstract

Purpose

Chiari malformations (CM) have been traditionally classified into four categories: I, II, III, and IV. In light of more recent understandings, variations of the CM have required a modification of this classification.

Methods

This article discusses the presentation, diagnostics, and treatment of the newer forms of hindbrain herniation associated with the CM type I.

Results

The CM 1 is a spectrum that includes some patients who do not fall into the exact category of this entity.

Conclusions

While CM have been categorically recognized as discrete and individual conditions, newer classifications such as CM 0 and CM 1.5 exhibit some degree of continuity with CM 1; however, they require distinct and separate classification as symptoms and treatments can vary among these clinical subtypes.
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Metadata
Title
Defining, diagnosing, clarifying, and classifying the Chiari I malformations
Authors
Stephen Bordes
Skyler Jenkins
R. Shane Tubbs
Publication date
01-10-2019
Publisher
Springer Berlin Heidelberg
Published in
Child's Nervous System / Issue 10/2019
Print ISSN: 0256-7040
Electronic ISSN: 1433-0350
DOI
https://doi.org/10.1007/s00381-019-04172-6

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