Published in:
01-04-2006
Sildenafil in Pulmonary Hypertension Secondary to Unilateral Agenesis of Pulmonary Artery
Published in: Pediatric Cardiology | Issue 2/2006
Login to get accessAbstract
Unilateral agenesis of the pulmonary artery (PA) is a rare anomaly that can lead to pulmonary hypertension (PHTN). We report the case of a 10-month-old female with agenesis of the left PA, ventricular septal defect, and patent ductus arteriosus who developed PHTN precluding surgical repair. The use of sildenafil decreased PA pressure and normalized pulmonary vascular resistance, after which surgery was successfully performed.