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Published in: Neuroradiology 4/2005

01-04-2005 | Interventional Neuroradiology

Ehlers–Danlos syndrome type IV and recurrent carotid-cavernous fistula: review of the literature, endovascular approach, technique and difficulties

Authors: H. A. Desal, F. Toulgoat, S. Raoul, B. Guillon, S. Bommard, E. Naudou-Giron, E. Auffray-Calvier, A. de Kersaint-Gilly

Published in: Neuroradiology | Issue 4/2005

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Abstract

We report the follow-up of a previously published case (Forlodou et al. Neuroradiology 38:595–597, 1996) of carotido-cavernous fistulas (CCFs) in a patient presenting with type IV Ehlers–Danlos syndrome (EDS 4) that were successfully treated twice by an endovascular approach. Initial treatment with a detachable balloon was in 1994 for a right CCF, and, 8 years later, a left CCF was treated by selective transarterial occlusion of the cavernous sinus with coils. Unfortunately, the patient suffered from a spontaneous post-operative intracranial haemorrhage in the left hemisphere and died. Review of the literature, technical considerations for bilateral CCF and complication are discussed.
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Metadata
Title
Ehlers–Danlos syndrome type IV and recurrent carotid-cavernous fistula: review of the literature, endovascular approach, technique and difficulties
Authors
H. A. Desal
F. Toulgoat
S. Raoul
B. Guillon
S. Bommard
E. Naudou-Giron
E. Auffray-Calvier
A. de Kersaint-Gilly
Publication date
01-04-2005
Publisher
Springer-Verlag
Published in
Neuroradiology / Issue 4/2005
Print ISSN: 0028-3940
Electronic ISSN: 1432-1920
DOI
https://doi.org/10.1007/s00234-005-1378-4

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