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Endocrine Pathology
Published in: Endocrine Pathology 1/2013

01-03-2013

Intraductal Polypoid Lipid-Rich Neuroendocrine Tumor of the Pancreas with Entrapped Ductules: Case Report and Review of the Literature

Authors: Jaclyn Frances Hechtman, Bernardo Franssen, Daniel M. Labow, Ronald E. Gordon, Christopher J. DiMaio, Eric J. Wilck, Gonzalo Carrasco-Avino, Hongfa Zhu

Published in: Endocrine Pathology | Issue 1/2013

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Abstract

Pancreatic neuroendocrine tumors of the main pancreatic duct are rare and usually small due to symptoms of pancreatic duct obstruction. We present a case of a large (3 cm), well-differentiated (G1) lipid-rich polypoid neuroendocrine tumor of the pancreas completely occluding the main pancreatic duct with non-neoplastic-entrapped ductules and CK19 positivity. Clinical, radiological, gross, microscopic, immunohistochemical, and ultrastructural findings are discussed. The literature pertaining to the unique features of this case is reviewed including clinical and pathologic pitfalls and the possible etiologic and prognostic significance of these findings.
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Metadata
Title
Intraductal Polypoid Lipid-Rich Neuroendocrine Tumor of the Pancreas with Entrapped Ductules: Case Report and Review of the Literature
Authors
Jaclyn Frances Hechtman
Bernardo Franssen
Daniel M. Labow
Ronald E. Gordon
Christopher J. DiMaio
Eric J. Wilck
Gonzalo Carrasco-Avino
Hongfa Zhu
Publication date
01-03-2013
Publisher
Springer US
Published in
Endocrine Pathology / Issue 1/2013
Print ISSN: 1046-3976
Electronic ISSN: 1559-0097
DOI
https://doi.org/10.1007/s12022-012-9231-x

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