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Clinical Rheumatology
Published in: Clinical Rheumatology 1/2004

01-02-2004 | Case Report

Inflammatory myopathy in a patient with cutaneous findings of pityriasis rubra pilaris: a case of Wong’s dermatomyositis

Authors: Roberto Caporali, Lorenzo Cavagna, Mario Bellosta, Laura Bogliolo, Carlomaurizio Montecucco

Published in: Clinical Rheumatology | Issue 1/2004

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Abstract

We report the case of a 46-year-old woman presenting cutaneous lesions similar to those of pityriasis rubra pilaris, characterized by diffuse scaling erythroderma and palmoplantar keratoderma; skin biopsy showed follicular hyperkeratosis with a perivascular lymphocytic infiltrate. One year later she developed an inflammatory myopathy; on the basis of clinical features, a diagnosis of dermatomyositis was made. Treatment with prednisone and hydroxychloroquine led to complete control of the cutaneous and muscular involvement, which was maintained during prednisone tapering.
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Metadata
Title
Inflammatory myopathy in a patient with cutaneous findings of pityriasis rubra pilaris: a case of Wong’s dermatomyositis
Authors
Roberto Caporali
Lorenzo Cavagna
Mario Bellosta
Laura Bogliolo
Carlomaurizio Montecucco
Publication date
01-02-2004
Publisher
Springer-Verlag
Published in
Clinical Rheumatology / Issue 1/2004
Print ISSN: 0770-3198
Electronic ISSN: 1434-9949
DOI
https://doi.org/10.1007/s10067-003-0807-1

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