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Published in: Pediatric Surgery International 7/2017

01-07-2017 | Original Article

Improving the rigour of VACTERL screening for neonates with anorectal malformations

Authors: Richard John England, Bala Eradi, Govind V. Murthi, Jonathan Sutcliffe

Published in: Pediatric Surgery International | Issue 7/2017

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Abstract

Purpose

Screening investigations for the vertebral, anorectal, cardiac, tracheo-oesophageal, renal and limb (VACTERL) association form an important part of the management of neonates with anorectal malformations (ARMs). We developed a proforma to define investigations and indications for referral. The aim of the current study was to determine if the proforma could improve screening rigour.

Methods

Four centres performed a 3-year retrospective audit of neonates with ARM. Following introduction of a proforma, the same data were collected prospectively for consecutive neonates over a further 2 years. The appropriate investigation of each component of the VACTERL association and the corresponding referral required for each abnormal result were defined. The proportion of patients undergoing appropriate investigation and referral was compared against these standards. An audit standard of 90% was set for each criteria.

Results

Prior to implementation of the proforma, 86 patients were audited, with a further 69 patients after. The audit standard was met in 7 criteria before introduction of the proforma in comparison to 10 criteria afterwards.

Conclusion

The completeness of VACTERL screening and its documentation improved following introduction of the proforma. Performance remains imperfect. Review of specific criteria (such as definition of vertebral body screening) will help address this.
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Metadata
Title
Improving the rigour of VACTERL screening for neonates with anorectal malformations
Authors
Richard John England
Bala Eradi
Govind V. Murthi
Jonathan Sutcliffe
Publication date
01-07-2017
Publisher
Springer Berlin Heidelberg
Published in
Pediatric Surgery International / Issue 7/2017
Print ISSN: 0179-0358
Electronic ISSN: 1437-9813
DOI
https://doi.org/10.1007/s00383-017-4094-3

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