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Journal of Clinical Immunology
Published in: Journal of Clinical Immunology 3/2018

01-04-2018 | Letter to Editor

Immunologist’s Perspectives on Assessment and Management of Lung Disease in CVID: a Survey of the Membership of the Clinical Immunology Society and the European Society for Immunodeficiencies

Authors: Javeed Akhter, Cheryl A. Lefaiver, Christopher Scalchunes, Michael DiGirolamo, Klaus Warnatz

Published in: Journal of Clinical Immunology | Issue 3/2018

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Excerpt

Over 350 primary immunodeficiency diseases are currently recognized. Other than selective IgA deficiency, common variable immunodeficiency (CVID) is the most common primary immunodeficiency disease [1]. The prevalence of CVID is estimated to be one in 25,000, but this is at best an educated guess. An International Consensus Document (ICON) [2] has proposed a revised definition for CVID and compared it with the previously published criteria suggested by Ameratunga et al. [3]. The usual practice is to use simpler criteria proposed by the European Society of Immune Deficiency Disorders (ESID) and Pan-American Group for Immunodeficiency (PAGID) [4]. …
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Metadata
Title
Immunologist’s Perspectives on Assessment and Management of Lung Disease in CVID: a Survey of the Membership of the Clinical Immunology Society and the European Society for Immunodeficiencies
Authors
Javeed Akhter
Cheryl A. Lefaiver
Christopher Scalchunes
Michael DiGirolamo
Klaus Warnatz
Publication date
01-04-2018
Publisher
Springer US
Published in
Journal of Clinical Immunology / Issue 3/2018
Print ISSN: 0271-9142
Electronic ISSN: 1573-2592
DOI
https://doi.org/10.1007/s10875-018-0488-9

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