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Published in: Acta Neurochirurgica 1/2024

01-12-2024 | Hypotension | Case Report

Management of cervical CSF-venous fistula causing acute cognitive impairment and coma

Authors: Lalani Carlton Jones, Jan Hoffmann, Saamir Mohideen, Biba Stanton, Cristina Bleil, Tom Britton, Peter J. Goadsby, Bassel Zebian

Published in: Acta Neurochirurgica | Issue 1/2024

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Abstract

CSF-venous fistulas (CVFs) are increasingly recognised as a cause of spontaneous intracranial hypotension. They may present atypically including with brain sagging pseudo-dementia. Cervical CVFs are rare and their management can be difficult due to associated eloquent nerve roots. We report the case of a 49-year-old woman who presented with cognitive decline progressing to coma. Brain imaging showed features of spontaneous intracranial hypotension and a right C7 CVF was identified at digital subtraction and CT myelography. Initial treatment with CT-guided injection of fibrin sealant produced temporary improvement in symptoms before surgical treatment resulted in total clinical remission and radiological resolution.
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Metadata
Title
Management of cervical CSF-venous fistula causing acute cognitive impairment and coma
Authors
Lalani Carlton Jones
Jan Hoffmann
Saamir Mohideen
Biba Stanton
Cristina Bleil
Tom Britton
Peter J. Goadsby
Bassel Zebian
Publication date
01-12-2024
Publisher
Springer Vienna
Published in
Acta Neurochirurgica / Issue 1/2024
Print ISSN: 0001-6268
Electronic ISSN: 0942-0940
DOI
https://doi.org/10.1007/s00701-024-05935-0

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