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Clinical Rheumatology
Published in: Clinical Rheumatology 1/2010

01-01-2010 | Case Report

Hypertrophic pachymeningitis with MPO-ANCA-positive vasculitis

Authors: Taro Horino, Toshihiro Takao, Yoshinori Taniguchi, Yoshio Terada

Published in: Clinical Rheumatology | Issue 1/2010

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Abstract

A 75-year-old man presented with headache, right facial palsy, and left hemiparesis. Because of elevated myeloperoxidase-antineutrophil cytoplasmic antibody (MPO-ANCA) titers and findings from magnetic resonance imaging (MRI) which were compatible with hypertrophic pachymeningitis (HP), he was diagnosed with MPO-ANCA-positive HP. He was treated with the combination therapy of steroid and cyclophosphamide (CY), leading to good prognosis. We present a case of HP associated with MPO-ANCA-positive vasculitis and emphasize the importance of MPO-ANCA tests as a predictable factor for relapse of the disease in order to start earlier treatment for the disease.
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Metadata
Title
Hypertrophic pachymeningitis with MPO-ANCA-positive vasculitis
Authors
Taro Horino
Toshihiro Takao
Yoshinori Taniguchi
Yoshio Terada
Publication date
01-01-2010
Publisher
Springer-Verlag
Published in
Clinical Rheumatology / Issue 1/2010
Print ISSN: 0770-3198
Electronic ISSN: 1434-9949
DOI
https://doi.org/10.1007/s10067-009-1269-x

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