Published in:
01-09-2019 | Case Report
Hanging Undifferentiated Embryonal Sarcoma of the Liver in Adult: an Unusual Presentation of an Aggressive Tumor
Authors:
Narendra Pandit, Kunal Bikram Deo, Lokesh Shekher Jaiswal, Anju Pradhan, Shailesh Adhikary
Published in:
Journal of Gastrointestinal Cancer
|
Issue 3/2019
Login to get access
Excerpt
Undifferentiated embryonal sarcoma of the liver (UESL) is a rare, highly aggressive hepatic neoplasm of mesenchymal origin seen almost exclusively in pediatric population [
1]. It was termed UESL for the first time by Stocker et al. in 1978 [
2]. This disease is very rare in adults with less than 70 cases reported in English literature [
3‐
5]. Though the tumor usually presents as a large liver tumor in an adult, a giant (> 10 cm) and hanging tumor arising from the Reidel’s lobe of the liver over a narrow stalk is very unusual and has not been reported in literature to date. We describe a case of a 29-year-old young female with a short clinical course and resectable hanging UESL, but unfortunately developed early recurrence despite R0 resection, signifying a poor prognosis disease. …