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Published in: Journal of Gastrointestinal Cancer 2/2020

01-06-2020 | Gastrointestinal Stromal Tumor | Case Report

Malignant Spindle Cell Neoplasm of Intestine: a Rare Case Report

Authors: Jyotsna Naresh Bharti, Kavita Sharma, Subhash Soni, Deepsikha Dharamsaktu

Published in: Journal of Gastrointestinal Cancer | Issue 2/2020

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Excerpt

Gastrointestinal stromal tumors (GISTs) are uncommon tumors accounting for 1% of all gastrointestinal tract (GIT) neoplasms [1]. GISTs are rare form of soft tissue sarcoma of the GIT. Two thirds of the GISTs are located in stomach while one fourth develops in the small intestine [2, 3]. The incidence of the GIST is very low, that is, 2 in 1,00,000, while jejunal GIST is extremely rare accounting for 0.1–3% of all GIT tumors [4]. The present discussion is limited to the small percentage which is found arising primarily from mesodermal tissue, the so-called spindle-cell tumors [24]. The typical subdivisions of this group—the neurinoma or neurofibroma, the leiomyoma, and the fibroma—are histologically well defined. Gastrointestinal stromal tumors (GISTs) are the most common mesenchymal tumors of the stomach with an incidence of 33–63% [1, 5, 6]. …
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Metadata
Title
Malignant Spindle Cell Neoplasm of Intestine: a Rare Case Report
Authors
Jyotsna Naresh Bharti
Kavita Sharma
Subhash Soni
Deepsikha Dharamsaktu
Publication date
01-06-2020
Publisher
Springer US
Published in
Journal of Gastrointestinal Cancer / Issue 2/2020
Print ISSN: 1941-6628
Electronic ISSN: 1941-6636
DOI
https://doi.org/10.1007/s12029-019-00309-7

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