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Published in: World Journal of Surgical Oncology 1/2004

Open Access 01-12-2004 | Case report

Gastric T-cell lymphoma associated with hemophagocytic syndrome

Authors: Rika Fukui, Fumitake Hata, Takahiro Yasoshima, Ryuuichi Denno, Minoru Okazaki, Kiyoshi Kasai, Masaaki Sato, Toshio Homma, Keisuke Ohno, Yoshiyuki Yanai, Katsuya Sogahata, Hidefumi Nishimori, Koichi Hirata

Published in: World Journal of Surgical Oncology | Issue 1/2004

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Abstract

Background

Lymphoma-associated hemophagocytic syndrome (LAHS) occurs in mostly extra nodal non-Hodgkin's lymphoma. LAHS arising from gastrointestinal lymphoma has never been reported. Here we report a case of gastric T-cell lymphoma-associated hemophagocytic syndrome.

Case presentation

A 51-year-old woman presented with pain, redness of breasts, fever and hematemesis. Hematological examination revealed anemia. Gastroscopy revealed small bleeding ulcers in the stomach and the computed tomography scan showed liver tumor. She underwent total gastrectomy for gastrointestinal bleeding and the histopathology revealed gastric T-cell lymphoma. She continued to bleed from the anastomosis and died on the 8th postoperative day. Autopsy revealed it to be a LAHS.

Conclusions

If Hemophagocytic syndrome (HPS) occurs in lymphoma of the gastrointestinal tract, bleeding from the primary lesion might be uncontrollable. Early diagnosis and appropriate treatment are needed for long-term survival.
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Metadata
Title
Gastric T-cell lymphoma associated with hemophagocytic syndrome
Authors
Rika Fukui
Fumitake Hata
Takahiro Yasoshima
Ryuuichi Denno
Minoru Okazaki
Kiyoshi Kasai
Masaaki Sato
Toshio Homma
Keisuke Ohno
Yoshiyuki Yanai
Katsuya Sogahata
Hidefumi Nishimori
Koichi Hirata
Publication date
01-12-2004
Publisher
BioMed Central
Published in
World Journal of Surgical Oncology / Issue 1/2004
Electronic ISSN: 1477-7819
DOI
https://doi.org/10.1186/1477-7819-2-34

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