Encyclopedia of autoimmune pancreatitis: this is all we need

Excerpt

Autoimmune pancreatitis (AIP) is a pancreatic inflammatory disease characterized by pancreatic swelling that requires differentiation from pancreatic cancer. In Japan, the majority of patients are type 1 AIP, which is diagnosed as a partial phenotype of IgG4-related disease, but there are also patients with type 2 AIP, which is not associated with increased serum IgG4. It has also been reported that IgG4-related disease is associated with various inflammatory changes not only in the pancreas but also in multiple organs as other organ involvement (OOI). Diagnostic criteria of AIP were published in the International Consensus Diagnostic Criteria (ICDC) and the clinical diagnostic criteria published by the Japanese Pancreas Society in 2018 (JPS2018), but the pathophysiology and diagnostic criteria of AIP are complicated [1, 2]. …