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The Egyptian Journal of Neurology, Psychiatry and Neurosurgery

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Open Access 01-12-2021 | Electroencephalography | Research

Rasmussen syndrome in a tropical environment: a study of six (6) observations

Authors: Carlos Othon Guelngar, Touré Mohamed Lamine, Barry Mamadou Ciré, Diakité Mamady, Konaté Mahadi, Djibo Hamani Bachir Abdoul, Sakadi Foksouna, Djibo Hassane Fatimata, Camara Naby, Kassa Dago François, Bah Fatimatou Korka, Camara Doussou, Millimono Victorine, Condé Salematou, Sakho Aminata, Diallo Mohamed Tafsir, Barry Souleymane Djigué, Diallo Mamadou Saliou, Soumah Fodé Mohamed, Sanni Yaya Aminou, Douna Granga Daouya, Rafkat Said Abdallah, Konaté Mamady, Diallo Souleymane Mbara, Cissé Fodé Abass, Cissé Amara

Published in: The Egyptian Journal of Neurology, Psychiatry and Neurosurgery | Issue 1/2021

Abstract

Background

In sub-Saharan Africa, encephalitis of various etiologies is a major public health problem and Rasmussen syndrome is rarely diagnosed due to under-medicalization. The objective of this study is to describe the clinical and neuroradiological forms, especially since this affection is little known in sub-Saharan Africa as evidenced by the scarcity of publications.

Results

A retrospective, descriptive and analytical study of six (6) cases of Rasmussen syndrome, shows that it is an unrecognized disease in Africa. Men were more represented with a frequency of 67% with a young age. The clinical picture dominated by 100% seizures, mental deterioration and hemiparesis. The etiology is still questionable, probably autoimmune in our study.

Conclusion

Rasmussen syndrome accounts for 3% in 219 patients hospitalized for epileptic conditions. This study shows a clinical profile dominated by recurrent epileptic seizures refractory to the drugs Phenobarbital, Valproic Acid and Carbamazepine, the only antiepileptics available in the country. These results are valid for therapeutic and prognostic discussion.

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Title: Rasmussen syndrome in a tropical environment: a study of six (6) observations
Authors: Carlos Othon Guelngar
Touré Mohamed Lamine
Barry Mamadou Ciré
Diakité Mamady
Konaté Mahadi
Djibo Hamani Bachir Abdoul
Sakadi Foksouna
Djibo Hassane Fatimata
Camara Naby
Kassa Dago François
Bah Fatimatou Korka
Camara Doussou
Millimono Victorine
Condé Salematou
Sakho Aminata
Diallo Mohamed Tafsir
Barry Souleymane Djigué
Diallo Mamadou Saliou
Soumah Fodé Mohamed
Sanni Yaya Aminou
Douna Granga Daouya
Rafkat Said Abdallah
Konaté Mamady
Diallo Souleymane Mbara
Cissé Fodé Abass
Cissé Amara
Publication date: 01-12-2021
Publisher: Springer Berlin Heidelberg
Keywords: Electroencephalography
Encephalitis
Epilepsy
Epileptic Seizure
Magnetic Resonance Imaging
Magnetic Resonance Imaging
Focal Seizure
Published in: The Egyptian Journal of Neurology, Psychiatry and Neurosurgery / Issue 1/2021
Electronic ISSN: 1687-8329
DOI: https://doi.org/10.1186/s41983-021-00409-x

Keynote webinar | Spotlight on medication adherence

Springer Medicine

Rasmussen syndrome in a tropical environment: a study of six (6) observations

Abstract

Background

Results

Conclusion

Keynote webinar | Spotlight on medication adherence

Springer Medicine

Abstract

Background

Results

Conclusion

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