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20-01-2023 | Dysphagia | Clinical Conundrum

A Case of Progressive Ataxia, Dysphagia, and Dysarthria Caused by a Rare Disease, and Treatment with Lingual Resistance Training

Authors: Mari Nakao-Kato, Shin-Ichi Izumi, Yutaka Maeno, Catriona M. Steele

Published in: Dysphagia | Issue 3/2023

Excerpt

A 55-year-old man was referred to the outpatient clinic of our rehabilitation department by a neurologist for dysphagia and dysarthria. At first visit, he complained of coughing at meals and colored sputum appearing 30 min after coffee intake. On the repetitive saliva swallowing test (RSST: normal ≥ 3 dry swallows in 30 s) [1], he was only able to generate 2 dry swallows in 30 s (average of three trials). The modified water swallow test (MWST), which involves observation for dyspnea, cough, or altered voice quality after swallowing sips of water [2], revealed coughing and a wet hoarse voice after the first 3 ml trial. The patient presented with progressive ataxia and dysarthria at 51 years of age. He had a history of falls at home and had injured his medial collateral ligament (LCL) at the age of 49. The frequency of falls had increased since then. On family history, his second son had severe intellectual and developmental disability. …

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Title: A Case of Progressive Ataxia, Dysphagia, and Dysarthria Caused by a Rare Disease, and Treatment with Lingual Resistance Training
Authors: Mari Nakao-Kato
Shin-Ichi Izumi
Yutaka Maeno
Catriona M. Steele
Publication date: 20-01-2023
Publisher: Springer US
Keywords: Dysphagia
Dysphagia
Dysarthria
Dysphagia
Published in: Dysphagia / Issue 3/2023
Print ISSN: 0179-051X
Electronic ISSN: 1432-0460
DOI: https://doi.org/10.1007/s00455-022-10551-0

At a glance: The STEP trials

Springer Medicine

A Case of Progressive Ataxia, Dysphagia, and Dysarthria Caused by a Rare Disease, and Treatment with Lingual Resistance Training

Excerpt

At a glance: The STEP trials

Springer Medicine

Excerpt

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