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Published in: HAND 3/2013

01-09-2013 | Case Reports

Dorsal radiocarpal dislocation in a patient with Goldenhar syndrome: case report

Authors: Johnathan A. Bernard, Andres O’Daly, Dawn M. LaPorte

Published in: HAND | Issue 3/2013

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Abstract

Background

Fracture–dislocations of the carpus are rare, generally occurring after high-energy trauma. Goldenhar syndrome is among a group of genetic abnormalities associated with radial limb defects. We present a case of a dorsal radiocarpal dislocation in a patient with Goldenhar syndrome after a low-energy fall. To our knowledge, there has been no previous report of radiocarpal dislocation in the setting of Goldenhar syndrome.

Methods

This patient with Goldenhar syndrome had a dorsal radiocarpal dislocation in the setting of an absent scaphoid and dysplastic distal radius. A computed tomography scan, recognized as a useful modality to evaluate the wrist and scaphoid, was used to rule out any other osseous trauma or avulsion fractures.

Results

Closed reduction and 6 weeks of immobilization resulted in a successful treatment.

Conclusions

The incidence of radiocarpal dislocations in patients with Goldenhar syndrome and the appropriate long-term treatment for patients with Goldenhar syndrome with radiocarpal dislocations require further investigation.
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Metadata
Title
Dorsal radiocarpal dislocation in a patient with Goldenhar syndrome: case report
Authors
Johnathan A. Bernard
Andres O’Daly
Dawn M. LaPorte
Publication date
01-09-2013
Publisher
Springer US
Published in
HAND / Issue 3/2013
Print ISSN: 1558-9447
Electronic ISSN: 1558-9455
DOI
https://doi.org/10.1007/s11552-013-9495-8

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