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Published in: World Journal of Surgical Oncology 1/2006

Open Access 01-12-2006 | Case report

Desmoid tumor in Gardner's Syndrome presented as acute abdomen

Authors: Andreas Hatzimarkou, Dimitrios Filippou, Vasilios Papadopoulos, Georgios Filippou, Spiros Rizos, Panagiotis Skandalakis

Published in: World Journal of Surgical Oncology | Issue 1/2006

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Abstract

Background

Gardner's syndrome can occasionally be complicated with intra-abdominal desmoid tumor. These tumors usually remain asymptomatic but can exhibit symptoms due to intestinal, vascular and ureteral compression and obstruction.

Case presentation

A rare case of a 41-year-old male patient with Gardner's syndrome complicated with intra-abdominal desmoid tumor, which first presented as acute abdomen, is presented.

Conclusion

Extra-abdominal manifestations of Gardner's syndrome along with a palpable abdominal mass would raise suspicion for the presence of a desmoid tumor in the majority of cases. In life-threatening cases, surgical treatment should be considered as a palliative approach, though the extent of excision remains debatable
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Metadata
Title
Desmoid tumor in Gardner's Syndrome presented as acute abdomen
Authors
Andreas Hatzimarkou
Dimitrios Filippou
Vasilios Papadopoulos
Georgios Filippou
Spiros Rizos
Panagiotis Skandalakis
Publication date
01-12-2006
Publisher
BioMed Central
Published in
World Journal of Surgical Oncology / Issue 1/2006
Electronic ISSN: 1477-7819
DOI
https://doi.org/10.1186/1477-7819-4-18

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