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Journal of Clinical Immunology
Published in: Journal of Clinical Immunology 4/2015

01-05-2015 | Brief Communication

Common Variable Immunodeficiency and Pulmonary Amyloidosis: A Case Report

Authors: Sevket Arslan, Ramazan Ucar, Dudu Mehmet Yavsan, Hasan Esen, Emin Maden, Ismail Reisli, Ahmet Zafer Calıskaner

Published in: Journal of Clinical Immunology | Issue 4/2015

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Abstract

Common variable immunodeficiency is the most common symptomatic primary immune deficiency characterized by hypogammaglobulinemia, recurrent infections, and increased risk of autoimmune disease and malignancy. Secondary amyloidosis develops from chronic inflammatory conditions. The co-existence of CVID (especially in patients with bronchiectasis) and secondary amyloidosis has been reported rarely. We describe the first case of pulmonary hypertension secondary to pulmonary amyloidosis in a patient with CVID.
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Metadata
Title
Common Variable Immunodeficiency and Pulmonary Amyloidosis: A Case Report
Authors
Sevket Arslan
Ramazan Ucar
Dudu Mehmet Yavsan
Hasan Esen
Emin Maden
Ismail Reisli
Ahmet Zafer Calıskaner
Publication date
01-05-2015
Publisher
Springer US
Published in
Journal of Clinical Immunology / Issue 4/2015
Print ISSN: 0271-9142
Electronic ISSN: 1573-2592
DOI
https://doi.org/10.1007/s10875-015-0151-7

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