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Published in:

01-02-2006

Coincidence of Long QT Syndrome and Propionic Acidemia

Authors: B. Kakavand, V.A. Schroeder, T. G. Di Sessa

Published in: Pediatric Cardiology | Issue 1/2006

Abstract

Propionic acidemia and long QT syndrome (LQTS) are rare disorders. In addition, both conditions are potentially lethal. The patient presented in this article was initially diagnosed with propionic acidemia. Incidentally, she was found to have LQTS on electrocardiogram and verified by stress test and epinephrine challenge. Although the patient was asymptomatic and arrhythmia free, we started her on atenolol. This is the first report of the association between LQTS and propionic acidemia.

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Title: Coincidence of Long QT Syndrome and Propionic Acidemia
Authors: B. Kakavand
V.A. Schroeder
T. G. Di Sessa
Publication date: 01-02-2006
Publisher: Springer New York
Published in: Pediatric Cardiology / Issue 1/2006
Print ISSN: 0172-0643
Electronic ISSN: 1432-1971
DOI: https://doi.org/10.1007/s00246-005-1129-7

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