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Child's Nervous System
Published in: Child's Nervous System 2/2021

01-02-2021 | Chondrosarcoma | Case Report

Intracranial extra-axial mesenchymal chondrosarcoma in a 16-month-old patient with a literature review of pediatric patients

Authors: Özlem Yapıcıer, Abdel Rahman Nanah, Mevlüt Özgür Taskapılıoglu, Mustafa Kemal Demir

Published in: Child's Nervous System | Issue 2/2021

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Abstract

Mesenchymal chondrosarcoma is a rare high-grade malignant subtype of chondrosarcoma that is characterized by undifferentiated, round, or spindled mesenchymal cells, interspersed with islands of hyaline cartilage. We report a primary intracranial extra-axial mesenchymal chondrosarcoma in a 16-month-old patient with a review of the literature focusing on intracranial extra-axial MCs with or without skull involvement in pediatric patients, including differential diagnosis. The patient was admitted with a swelling in the right temporooccipital region. There was intracranial extra-dural extension of the mass, which abuts the neural parenchyma without any invasion. A complete tumor resection was performed. Pathological diagnosis was mesenchymal chondrosarcoma. The patient was free of symptoms after surgery.
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Metadata
Title
Intracranial extra-axial mesenchymal chondrosarcoma in a 16-month-old patient with a literature review of pediatric patients
Authors
Özlem Yapıcıer
Abdel Rahman Nanah
Mevlüt Özgür Taskapılıoglu
Mustafa Kemal Demir
Publication date
01-02-2021
Publisher
Springer Berlin Heidelberg
Keyword
Chondrosarcoma
Published in
Child's Nervous System / Issue 2/2021
Print ISSN: 0256-7040
Electronic ISSN: 1433-0350
DOI
https://doi.org/10.1007/s00381-020-04652-0

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