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01-12-2005 | Case Report

Cherubism associated with neurofibromatosis type 1, and multiple osteolytic lesions of both femurs: A previously undescribed association of findings

Authors: Francisco J. Martínez-Tello, Palmira Manjón-Luengo, Manuel Martin-Pérez, Santiago Montes-Moreno

Published in: Skeletal Radiology | Issue 12/2005

Abstract

We present a patient with neurofibromatosis type 1, with the clinical, radiological and histological features of cherubism mandibular lesions, and multiple osteolytic, geographic lesions in both femurs, consistent with multiple non-ossifying fibromas. We have been unable to find a similar case in the world literature. We discuss our findings in relationship with a number of syndromes that present clinical, radiological or pathological similarities.

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Title: Cherubism associated with neurofibromatosis type 1, and multiple osteolytic lesions of both femurs: A previously undescribed association of findings
Authors: Francisco J. Martínez-Tello
Palmira Manjón-Luengo
Manuel Martin-Pérez
Santiago Montes-Moreno
Publication date: 01-12-2005
Publisher: Springer-Verlag
Published in: Skeletal Radiology / Issue 12/2005
Print ISSN: 0364-2348
Electronic ISSN: 1432-2161
DOI: https://doi.org/10.1007/s00256-005-0938-3

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Cherubism associated with neurofibromatosis type 1, and multiple osteolytic lesions of both femurs: A previously undescribed association of findings

Abstract

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Abstract

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