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Published in: Thrombosis Journal 1/2020

01-12-2020 | Cardiomyopathy | Case report

Superior vena cava thrombosis and dilated cardiomyopathy as initial presentations of Behcet’s disease

Authors: Ahmed M. Elzanaty, Mohammed T. Awad, Ashu Acharaya, Ebrahim Sabbagh, Eman Elsheikh, Moshrik AbdAlamir

Published in: Thrombosis Journal | Issue 1/2020

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Abstract

Background

Bechet’s disease (BD) is a relatively rare disease that causes recurrent oral and genital ulcers in addition to a variety of systemic manifestations. Concomitant superior-vena-cava (SVC) thrombosis and cardiac involvement with dilated cardiomyopathy (DCM) as initial presentations for BD is considered rare.

Case presentation

A 32-year-old-man presenting with intractable headaches and dyspnea. He was later diagnosed with SVC thrombosis and DCM. A diagnosis of BD was made after detailed history-taking.

Conclusions

Cardiovascular manifisations can be the initial presentation of BD. We aim to highlight the importance of early clinical recognition of BD as a cause of DCM and SVC thrombosis.
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Metadata
Title
Superior vena cava thrombosis and dilated cardiomyopathy as initial presentations of Behcet’s disease
Authors
Ahmed M. Elzanaty
Mohammed T. Awad
Ashu Acharaya
Ebrahim Sabbagh
Eman Elsheikh
Moshrik AbdAlamir
Publication date
01-12-2020
Publisher
BioMed Central
Published in
Thrombosis Journal / Issue 1/2020
Electronic ISSN: 1477-9560
DOI
https://doi.org/10.1186/s12959-020-00225-y

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