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01-04-2021 | Astrocytoma | Case Report

A case of subependymal giant cell astrocytoma without tuberous sclerosis complex and review of the literature

Authors: Michael O’Rawe, Arjun S. Chandran, Stuti Joshi, Alexandre Simonin, Jason M. Dyke, Sharon Lee

Published in: Child's Nervous System | Issue 4/2021

Abstract

Subependymal giant cell astrocytoma (SEGA) is a World Health Organization (WHO) grade I tumor most commonly seen in the context of the underlying tuberous sclerosis complex (TSC). SEGA in the absence of TSC is exceedingly rare. We report the youngest known case of SEGA in the absence of genetic or phenotypic evidence of TSC with a 10-year follow-up. We discuss the literature surrounding isolated SEGA including an approach to diagnosis, management, and prognosis.

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Title: A case of subependymal giant cell astrocytoma without tuberous sclerosis complex and review of the literature
Authors: Michael O’Rawe
Arjun S. Chandran
Stuti Joshi
Alexandre Simonin
Jason M. Dyke
Sharon Lee
Publication date: 01-04-2021
Publisher: Springer Berlin Heidelberg
Keywords: Astrocytoma
Tuberous Sclerosis
Astrocytoma
Astrocytoma
Published in: Child's Nervous System / Issue 4/2021
Print ISSN: 0256-7040
Electronic ISSN: 1433-0350
DOI: https://doi.org/10.1007/s00381-020-04823-z

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A case of subependymal giant cell astrocytoma without tuberous sclerosis complex and review of the literature

Abstract

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