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Pediatric Cardiology
Published in: Pediatric Cardiology 2/2008

01-03-2008 | Case Report

Arrhythmogenic Right Ventricular Cardiomyopathy in an 11-Year-Old Girl and Typical Echocardiographic Features

Authors: Abdul Rahim Wong, Nabil AbdurRazak, Saad Mohammad Al-Hadlaq, Abdullah Salem Al-Jarallah

Published in: Pediatric Cardiology | Issue 2/2008

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Abstract

Arrhythmogenic right ventricular cardiomyopathy (ARVC) is a rare entity that affects children as well as adults. This is a genetic disorder that can be inherited and whose hallmark is fibrofatty replacement of ventricular muscle, especially of the right side, with ventricular arrhythmias and progressive heart failure. We describe a case of an 11-year-old Saudi girl with ARVC and the echocardiographic characteristics that had been highlighted by the Taskforce for ARVC, and we suggest that a concurrent criterion be added to aid further echo identification in children.
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Metadata
Title
Arrhythmogenic Right Ventricular Cardiomyopathy in an 11-Year-Old Girl and Typical Echocardiographic Features
Authors
Abdul Rahim Wong
Nabil AbdurRazak
Saad Mohammad Al-Hadlaq
Abdullah Salem Al-Jarallah
Publication date
01-03-2008
Publisher
Springer-Verlag
Published in
Pediatric Cardiology / Issue 2/2008
Print ISSN: 0172-0643
Electronic ISSN: 1432-1971
DOI
https://doi.org/10.1007/s00246-007-9082-2

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