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Published in: European Journal of Pediatrics 4/2009

01-04-2009 | Short Report

An unusual cause of gastric perforation in childhood: trichobezoar (Rapunzel syndrome). A case report

Authors: Orhan Koç, Fesih Doğan Yıldız, Adnan Narcı, Tolga Altuğ Şen

Published in: European Journal of Pediatrics | Issue 4/2009

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Abstract

Trichobezoars are hair balls found in the stomach and formed following trichitillomania and trichopaghia. Rapunzel syndrome is a rare condition in which the presence of giant trichobezoars causes mechanical obstruction. To date, only two cases of stomach perforation caused by trichobezoars have been reported among pediatric patients. We report a 14-year-old female patient who experienced nausea, vomiting and severe abdominal pain for 1 month. Physical examination revealed diffuse abdominal distension. Palpation detected a mobile and sensitive mass, 15 × 15 cm , which filled the upper quadrant. Urgent surgery revealed that the stomach was perforated by the trichobezoar ball. This trichobezoar mass was totally excised by expanding the perforation area. Conclusion This is the reported third case of gastric perforation caused by trichobezoar in a pediatric patient. Among acute abdominal cases, gastric perforation should remain a possibility in differential diagnosis.
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Metadata
Title
An unusual cause of gastric perforation in childhood: trichobezoar (Rapunzel syndrome). A case report
Authors
Orhan Koç
Fesih Doğan Yıldız
Adnan Narcı
Tolga Altuğ Şen
Publication date
01-04-2009
Publisher
Springer-Verlag
Published in
European Journal of Pediatrics / Issue 4/2009
Print ISSN: 0340-6199
Electronic ISSN: 1432-1076
DOI
https://doi.org/10.1007/s00431-008-0773-3

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