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World Journal of Surgical Oncology
Published in: World Journal of Surgical Oncology 1/2016

Open Access 01-12-2016 | Case report

A giant mucinous cystadenocarcinoma of the appendix: a case report and review of the literature

Authors: Hiroshi Nagata, Yuji Kondo, Kazushige Kawai, Soichiro Ishihara, Shinsuke Kazama, Takako Nirei, Daisuke Soma, Jun Yamada, Eiji Sunami, Joji Kitayama, Yoshiro Kubota, Toshiaki Watanabe

Published in: World Journal of Surgical Oncology | Issue 1/2016

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Abstract

Background

Mucinous cystadenocarcinoma is the second most common etiology of appendiceal mucocele. We report a relatively rare case of a giant appendiceal mucocele caused by mucinous cystadenocarcinoma, which occupied the entire abdomen of an adult woman.

Case presentation

A 63-year-old woman presented with a chief complaint of abdominal distention. Imaging studies showed a giant cystic mass occupying her entire abdomen. Laparotomy confirmed a giant appendiceal mucocele, and the patient underwent ileocecal resection. A mucinous deposit was not found in her abdominal cavity, and the ovaries were grossly normal bilaterally. The pathological diagnosis was mucinous adenocarcinoma with a low-grade mucinous neoplasm that invaded the subserosa. Regional lymph node metastasis was not found. She has had recurrence-free survival for 5 years.

Conclusions

The present case is the largest appendiceal cystadenocarcinoma ever reported. The optimal treatment of an appendiceal neoplasm requires further research based on consensus terminology of an appendiceal mucocele.
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Metadata
Title
A giant mucinous cystadenocarcinoma of the appendix: a case report and review of the literature
Authors
Hiroshi Nagata
Yuji Kondo
Kazushige Kawai
Soichiro Ishihara
Shinsuke Kazama
Takako Nirei
Daisuke Soma
Jun Yamada
Eiji Sunami
Joji Kitayama
Yoshiro Kubota
Toshiaki Watanabe
Publication date
01-12-2016
Publisher
BioMed Central
Published in
World Journal of Surgical Oncology / Issue 1/2016
Electronic ISSN: 1477-7819
DOI
https://doi.org/10.1186/s12957-016-0828-2

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