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01-01-2011 | Case Report

A case of cystic biliary atresia with an antenatally detected cyst: the possibility of changing from a correctable type with a cystic lesion (I cyst) to an uncorrectable one (IIId)

Authors: Kouji Masumoto, Hiroki Kai, Yoichiro Oka, Ryoko Otake, Toshiyuki Yoshizato, Shingo Miyamoto, Shinichi Hirose, Makoto Hamasaki, Kazuki Nabeshima, Akinori Iwasaki

Published in: Pediatric Surgery International | Issue 1/2011

Abstract

This report presents the case of a 6-day-old male with cystic biliary atresia (CBA), and the cyst was detected antenatally. Antenatal ultrasonography suggested the possibility of CBA or a choledochal cyst at 16 weeks’ gestation. However, the cyst disappeared during the later gestational period. The cyst was detected again by preoperative imaging. Surgical cholangiography at 30 days of age confirmed CBA, but the common hepatic duct (CHD) was extremely narrow. The histopathological findings revealed the partial obstruction of CHD. These findings suggest that correctable CBA (I cyst) may change into uncorrectable CBA (IIId).

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Title: A case of cystic biliary atresia with an antenatally detected cyst: the possibility of changing from a correctable type with a cystic lesion (I cyst) to an uncorrectable one (IIId)
Authors: Kouji Masumoto
Hiroki Kai
Yoichiro Oka
Ryoko Otake
Toshiyuki Yoshizato
Shingo Miyamoto
Shinichi Hirose
Makoto Hamasaki
Kazuki Nabeshima
Akinori Iwasaki
Publication date: 01-01-2011
Publisher: Springer-Verlag
Published in: Pediatric Surgery International / Issue 1/2011
Print ISSN: 0179-0358
Electronic ISSN: 1437-9813
DOI: https://doi.org/10.1007/s00383-010-2715-1

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A case of cystic biliary atresia with an antenatally detected cyst: the possibility of changing from a correctable type with a cystic lesion (I cyst) to an uncorrectable one (IIId)

Abstract

Keynote webinar | Spotlight on medication adherence

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Abstract

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