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Published in: Journal of Medical Case Reports 1/2009

Open Access 01-12-2009 | Case report

Visual impairment from fibrous dysplasia in a middle-aged African man: a case report

Authors: Charles O Bekibele, Olubayo A Fasola, Vickie N Okojie, Opeyemi O Komolafe, Olayiwola A Oluwasola, Jude K Emejulu, Ayotunde I Ajaiyeoba, Aderonke M Baiyeroju

Published in: Journal of Medical Case Reports | Issue 1/2009

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Abstract

Introduction

Fibrous dysplasia is a benign tumour of the bones and is a disease of unknown aetiology. This report discusses a case of proptosis and visual deterioration with associated bony mass involving the right orbit.

Case presentation

A 32-year-old Nigerian man of Yoruba ethnic origin presented to the eye clinic of our hospital with right-eye proptosis and visual deterioration of 7-year duration. Presentation was preceded by a history of trauma. Proptosis was preceded by trauma but was non-pulsatile with no thrill or bruit but was associated with bony orbital mass. The patient reported no weight loss. Examination of his right eye showed visual acuity of 6/60 with relative afferent pupillary defect. Fundal examination revealed optic atrophy. Computed tomography showed an expansile bony mass involving all the walls of the orbit. The bony orbital mass was diagnosed histologically as fibrous dysplasia. Treatment included orbital exploration and orbital shaping to create room for the globe and relieve pressure on the optic nerve.

Conclusion

Fibrous dysplasia should be considered in the differential diagnosis of slowly developing proptosis with associated visual loss in young adults.
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Metadata
Title
Visual impairment from fibrous dysplasia in a middle-aged African man: a case report
Authors
Charles O Bekibele
Olubayo A Fasola
Vickie N Okojie
Opeyemi O Komolafe
Olayiwola A Oluwasola
Jude K Emejulu
Ayotunde I Ajaiyeoba
Aderonke M Baiyeroju
Publication date
01-12-2009
Publisher
BioMed Central
Published in
Journal of Medical Case Reports / Issue 1/2009
Electronic ISSN: 1752-1947
DOI
https://doi.org/10.1186/1752-1947-3-14

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