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World Journal of Emergency Surgery

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Open Access 01-12-2010 | Case report

Unusual case of pancreatic inflammatory myofibroblastic tumor associated with spontaneous splenic rupture

Authors: Kamal S Hassan, Hector I Cohen, Fadi K Hassan, Shadi K Hassan

Published in: World Journal of Emergency Surgery | Issue 1/2010

Abstract

Background

Spontaneous splenic rupture considered a relatively rare but life threatening. The three commonest causes of spontaneous splenic rupture are malignant hematological diseases, viral infections and local inflammatory and neoplastic disorders. We describe a unique and unusual case of inflammatory myofibroblastic tumor of the tail of pancreas presented with massively enlarged spleen and spontaneous splenic rupture.

Case presentation

A 19 years old male patient with no significant past medical history presented to emergency room with abdominal pain and fatigue. Massively enlarged spleen was detected. Hypotension and rapid reduction of hemoglobin level necessitated urgent laparatomy. About 1.75 liters of blood were found in abdominal cavity. A large tumor arising from the tail of pancreas and local rupture of an enlarged spleen adjacent to the tumor were detected. Distal pancreatectomy and splenectomy were performed. To our knowledge, we report the first case of massively enlarged spleen that was complicated with spontaneous splenic rupture as a result of splenic congestion due to mechanical obstruction caused by an inflammatory myofibroblastic tumor of the tail of pancreas. A review of the literature is also presented.

Conclusion

Inflammatory myofibroblastic tumor of the tail of pancreas should be included in the differential diagnosis of the etiological causes of massively enlarged spleen and spontaneous splenic rupture.

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Title: Unusual case of pancreatic inflammatory myofibroblastic tumor associated with spontaneous splenic rupture
Authors: Kamal S Hassan
Hector I Cohen
Fadi K Hassan
Shadi K Hassan
Publication date: 01-12-2010
Publisher: BioMed Central
Published in: World Journal of Emergency Surgery / Issue 1/2010
Electronic ISSN: 1749-7922
DOI: https://doi.org/10.1186/1749-7922-5-28

At a glance: The ONWARDS insulin icodec trials

Springer Medicine

Unusual case of pancreatic inflammatory myofibroblastic tumor associated with spontaneous splenic rupture

Abstract

Background

Case presentation

Conclusion

At a glance: The ONWARDS insulin icodec trials

Springer Medicine

Abstract

Background

Case presentation

Conclusion

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