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European Archives of Oto-Rhino-Laryngology

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01-10-2018 | Otology

Unilateral congenital malformations of middle ear with intact external ear: a review of 64 cases

Authors: Chaoying Tang, Jishuai Zhang, Shiming Yang, Dongyi Han, Weiju Han

Published in: European Archives of Oto-Rhino-Laryngology | Issue 10/2018

Abstract

Objective

To describe the operative findings and surgical results of unilateral congenital middle ear malformations with intact external ear.

Methods

A retrospective review was performed on 64 patients with unilateral congenital middle ear malformations and intact external ear who underwent exploratory tympanotomy from 2011 to 2016. Demographic data, clinical data, high-resolution computed tomography findings, audiometric data and intraoperative findings were collected. Audiological evaluations before and 6 months after surgery were analyzed in 47 patients.

Results

The most common malformation were mobile stapes with missing incus long process and stapes suprastructure. The air conduction pure tone average was 58.9 ± 10.5 dB HL (range 34.4–78.1 dB HL) preoperatively and 28.8 ± 10.6 dB HL (range 9.4–55.6 dB HL) postoperatively (P = 0.000). Twenty-five cases (53.2%) acquired an air conduction hearing gain exceeding 30 dB. Mean air-bone gap (ABG) was 44.5 ± 9.4 dB (range 22.5–66.4 dB HL) before surgery and 15.6 ± 9.3 dB (range 0–35.6 dB) after surgery (P = 0.000) for an average gain of 28.8 ± 11.5 dB. Thirty-four cases (72.3%) showed a postoperative ABG of less than 20 dB, 15 had an ABG within 10 dB, and 4 had 0 dB ABG after operation. No significant difference was observed for air conduction hearing gain regarding age (P = 0.261) or types of malformations (mobile stapes footplate with or without a suprastructure anomaly, P = 0.058).

Conclusion

Unilateral congenital middle ear malformations with intact external ear can be complex and diverse. Functional ossiculoplasty for patients with unilateral congenital middle ear malformations can achieve good hearing outcomes.

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Title: Unilateral congenital malformations of middle ear with intact external ear: a review of 64 cases
Authors: Chaoying Tang
Jishuai Zhang
Shiming Yang
Dongyi Han
Weiju Han
Publication date: 01-10-2018
Publisher: Springer Berlin Heidelberg
Published in: European Archives of Oto-Rhino-Laryngology / Issue 10/2018
Print ISSN: 0937-4477
Electronic ISSN: 1434-4726
DOI: https://doi.org/10.1007/s00405-018-5099-9

Keynote webinar | Spotlight on medication adherence

Springer Medicine

Unilateral congenital malformations of middle ear with intact external ear: a review of 64 cases

Abstract

Objective

Methods

Results

Conclusion

Keynote webinar | Spotlight on medication adherence

Springer Medicine

Abstract

Objective

Methods

Results

Conclusion

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