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European Journal of Orthopaedic Surgery & Traumatology

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01-08-2018 | Up-to date Review and Case Report • SPINE - CERVICAL

Traumatic cervical spine injuries in a patient with pycnodysostosis

Authors: Khaled Zitouna, Myriam Jrad, Mehdi Miladi, Maher Barsaoui, Ghassen Drissi, Mohamed Lassaad Kanoun

Published in: European Journal of Orthopaedic Surgery & Traumatology | Issue 6/2018

Abstract

Pycnodysostosis is a rare hereditary disease, characterized by systemic bone sclerosis. Susceptibility to long bone fractures is characteristic, whereas vertebral fractures are extremely rare. We report a case of a 21-year-old man with a past history of pycnodysostosis and spontaneous leg fractures who was admitted in hospital for a neck pain after a banal fall. Radiological examination revealed C1–C2–C3 posterior arch fractures with a C3–C4 left articular fracture dislocation. A surgical stabilization was decided but refused by the patient. To the best of our knowledge, this is the first publication that reports pycnodysostosis with cervical spine traumatic staged injuries.

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Title: Traumatic cervical spine injuries in a patient with pycnodysostosis
Authors: Khaled Zitouna
Myriam Jrad
Mehdi Miladi
Maher Barsaoui
Ghassen Drissi
Mohamed Lassaad Kanoun
Publication date: 01-08-2018
Publisher: Springer Paris
Published in: European Journal of Orthopaedic Surgery & Traumatology / Issue 6/2018
Print ISSN: 1633-8065
Electronic ISSN: 1432-1068
DOI: https://doi.org/10.1007/s00590-018-2165-3

At a glance: The STEP trials

Springer Medicine

Traumatic cervical spine injuries in a patient with pycnodysostosis

Abstract

At a glance: The STEP trials

Springer Medicine

Abstract

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