Published in:
01-08-2003 | Case Report
Thoracic malignant peripheral nerve sheath tumour mimicking a pleural tumour: a rare pedunculated appearance
Authors:
Masahiro Komori, Hidetake Yabuuchi, Toshiro Kuroiwa, Yoshihisa Nagatoshi, Yukito Ichinose, Yoichi Hachitanda
Published in:
Pediatric Radiology
|
Issue 8/2003
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Abstract
A malignant peripheral nerve sheath tumour (MPNST) generally occurs in adults and often in patients with neurofibromatosis-1 (NF-1). We present a rare case of a huge thoracic MPNST arising from the intercostal nerve in a 12-year-old girl without NF-1. In addition to the unusual occurrence in a child without NF-1, MRI demonstrated a unique pedunculated appearance mimicking a pleural tumour. In this report, we present the CT and MRI findings of our case, together with the histopathological findings, and review previous reports.