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01-01-2018 | Case Report

The challenges of closing an ileostomy in patients with total intestinal aganglionosis after small bowel transplant

Authors: Fereshteh Salimi Jazi, Tiffany J. Sinclair, Chad M. Thorson, Ricardo Castillo, Andrew C. Bonham, Carlos O. Esquivel, Matias Bruzoni

Published in: Pediatric Surgery International | Issue 1/2018

Abstract

We present the case of a 14-year-old male with a history of small bowel transplantation for long segment Hirschsprung’s disease who underwent Duhamel ileorectal pull-through procedure. In post-transplant, the patient had no restrictions and was not TPN-dependent. To improve his quality of life, he and his family were interested in closing the ileostomy and undergoing pull-through surgery. The complexity of the case includes the presence of an aganglionic rectal segment—a short root of the mesentery due to the small bowel transplant—and significant immunosuppression. At the moment, he is continent, doing well, and has not had any remarkable complications.

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Title: The challenges of closing an ileostomy in patients with total intestinal aganglionosis after small bowel transplant
Authors: Fereshteh Salimi Jazi
Tiffany J. Sinclair
Chad M. Thorson
Ricardo Castillo
Andrew C. Bonham
Carlos O. Esquivel
Matias Bruzoni
Publication date: 01-01-2018
Publisher: Springer Berlin Heidelberg
Published in: Pediatric Surgery International / Issue 1/2018
Print ISSN: 0179-0358
Electronic ISSN: 1437-9813
DOI: https://doi.org/10.1007/s00383-017-4216-y

At a glance: The STEP trials

Springer Medicine

The challenges of closing an ileostomy in patients with total intestinal aganglionosis after small bowel transplant

Abstract

At a glance: The STEP trials

Springer Medicine

Abstract

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