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01-10-2011 | Short Commentary

Surviving stiff-person syndrome: a case report

Authors: Sharmilee Gnanapavan, Angela Vincent, Gavin Giovannoni

Published in: Journal of Neurology | Issue 10/2011

Abstract

Stiff-person syndrome (SPS) is a rare condition of progressive muscular rigidity and spasm, frequently accompanied by other autoimmune conditions, an association which has been further strengthened by the discovery of anti-GAD antibodies and the response of SPS to immunotherapies. Intravenous immunoglobulin (IVIg) is the mainstay therapy. Because of the rarity of the GAD antibody associated conditions, most of the information regarding treatment is case series and individual case reports. Here we describe the 15 year long management of a subject with SPS who has had a favourable outcome.

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Title: Surviving stiff-person syndrome: a case report
Authors: Sharmilee Gnanapavan
Angela Vincent
Gavin Giovannoni
Publication date: 01-10-2011
Publisher: Springer-Verlag
Published in: Journal of Neurology / Issue 10/2011
Print ISSN: 0340-5354
Electronic ISSN: 1432-1459
DOI: https://doi.org/10.1007/s00415-011-6015-z

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Surviving stiff-person syndrome: a case report

Abstract

Keynote webinar | Spotlight on medication adherence

Springer Medicine

Abstract

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