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Child's Nervous System

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01-03-2017 | Case Report

Surgical resection of large encephalocele: a report of two cases and consideration of resectability based on developmental morphology

Authors: Hideo Ohba, Satoshi Yamaguchi, Takashi Sadatomo, Masaaki Takeda, Manish Kolakshyapati, Kaoru Kurisu

Published in: Child's Nervous System | Issue 3/2017

Abstract

Introduction

The first-line treatment of encephalocele is reduction of herniated structures. Large irreducible encephalocele entails resection of the lesion. In such case, it is essential to ascertain preoperatively if the herniated structure encloses critical venous drainage.

Case reports

Two cases of encephalocele presenting with large occipital mass underwent magnetic resonance (MR) imaging. In first case, the skin mass enclosed the broad space containing cerebrospinal fluid and a part of occipital lobe and cerebellum. The second case had occipital mass harboring a large portion of cerebrum enclosing dilated ventricular space. Both cases had common venous anomalies such as split superior sagittal sinus and high-positioned torcular herophili. They underwent resection of encephalocele without subsequent venous congestion. We could explain the pattern of venous anomalies in encephalocele based on normal developmental theory.

Conclusion

Developmental theory connotes that major dural sinuses cannot herniate into the sac of encephalocele. Irrespective to its size, encephalocele can be resected safely at the neck without subsequent venous congestion.

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Title: Surgical resection of large encephalocele: a report of two cases and consideration of resectability based on developmental morphology
Authors: Hideo Ohba
Satoshi Yamaguchi
Takashi Sadatomo
Masaaki Takeda
Manish Kolakshyapati
Kaoru Kurisu
Publication date: 01-03-2017
Publisher: Springer Berlin Heidelberg
Published in: Child's Nervous System / Issue 3/2017
Print ISSN: 0256-7040
Electronic ISSN: 1433-0350
DOI: https://doi.org/10.1007/s00381-016-3290-0

At a glance: The STEP trials

Springer Medicine

Surgical resection of large encephalocele: a report of two cases and consideration of resectability based on developmental morphology

Abstract

Introduction

Case reports

Conclusion

At a glance: The STEP trials

Springer Medicine

Abstract

Introduction

Case reports

Conclusion

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