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Published in: Indian Journal of Otolaryngology and Head & Neck Surgery 1/2019

01-10-2019 | Clinical Report

Surgical Excision with Rotational Flap Reconstruction for Basosquamous Cell Carcinoma in Xeroderma Pigmentosa: A Case Report

Authors: Sharanabasappa Rudragouda Malipatil, Sriharsha Vijay Jonnalagadda

Published in: Indian Journal of Otolaryngology and Head & Neck Surgery | Special Issue 1/2019

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Abstract

Xeroderma pigmentosa (XP) is a rare autosomal recessive disorder which is characterized by a defect in nucleotide excision repair of DNA following exposure to UV radiation. This leads to hypersensitivity to sunlight causing pigmented skin lesions, photophobia and a 1000-fold increase in risk of developing cutaneous malignancies like basal cell carcinomas, squamous cell carcinomas and melanomas of head and neck. We present an interesting case of a 28 year old man with basosquamous cell carcinoma secondary to XP treated successfully with surgical excision and reconstruction with rotational flap technique.
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Metadata
Title
Surgical Excision with Rotational Flap Reconstruction for Basosquamous Cell Carcinoma in Xeroderma Pigmentosa: A Case Report
Authors
Sharanabasappa Rudragouda Malipatil
Sriharsha Vijay Jonnalagadda
Publication date
01-10-2019
Publisher
Springer India
Published in
Indian Journal of Otolaryngology and Head & Neck Surgery / Issue Special Issue 1/2019
Print ISSN: 2231-3796
Electronic ISSN: 0973-7707
DOI
https://doi.org/10.1007/s12070-018-1508-z

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