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Published in: Heart and Vessels 2/2014

Open Access 01-03-2014 | Case Report

Subsequent shunt closure after targeted medical therapy can be an effective strategy for secundum atrial septal defect with severe pulmonary arterial hypertension: two case reports

Strategy for ASD with Severe PAH

Authors: Yu Taniguchi, Noriaki Emoto, Kazuya Miyagawa, Kazuhiko Nakayama, Hiroto Kinutani, Hidekazu Tanaka, Toshiro Shinke, Kenji Okada, Yutaka Okita, Ken-ich Hirata

Published in: Heart and Vessels | Issue 2/2014

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Abstract

Secundum atrial septal defect (ASD) is the most common form of congenital heart disease in adults. Surgical and transcatheter closures of ASD are widely accepted therapeutic approaches. In patients with severe pulmonary arterial hypertension (PAH), however, the closure of the defect is still controversial. We report two cases of ASD patients with severe PAH successfully repaired subsequent to effective medical therapy. Subsequent shunt closure after targeted medical therapy can be an effective strategy in selected ASD patients with severe PAH.
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Metadata
Title
Subsequent shunt closure after targeted medical therapy can be an effective strategy for secundum atrial septal defect with severe pulmonary arterial hypertension: two case reports
Strategy for ASD with Severe PAH
Authors
Yu Taniguchi
Noriaki Emoto
Kazuya Miyagawa
Kazuhiko Nakayama
Hiroto Kinutani
Hidekazu Tanaka
Toshiro Shinke
Kenji Okada
Yutaka Okita
Ken-ich Hirata
Publication date
01-03-2014
Publisher
Springer Japan
Published in
Heart and Vessels / Issue 2/2014
Print ISSN: 0910-8327
Electronic ISSN: 1615-2573
DOI
https://doi.org/10.1007/s00380-013-0351-0

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