Published in:
01-06-2007 | Case Report
Staged resection for a ruptured hepatoblastoma: a 6-year follow-up
Authors:
Mansoor Ahmed Madanur, Narendra Battula, Mark Davenport, Anil Dhawan, Mohamed Rela
Published in:
Pediatric Surgery International
|
Issue 6/2007
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Abstract
Hepatoblastoma (HB) is a rare germ cell tumour of childhood usually presenting with progressive abdominal distention. However, presentation as acute abdomen is a rare occurrence and is secondary to spontaneous rupture. This presentation carries high mortality. To our knowledge, six cases of ruptured hepatoblastoma have previously been reported, although the long-term outcome has not been clear. We report a case of ruptured HB who was managed by initial control of haemorrhage by laparotomy followed by chemotherapy with high-risk hepatoblastoma protocol as per SIOPEL 2 (cisplatin, carboplatin and doxorubicin) and a staged hepatectomy 5 months later. Patient is currently disease free at 6-year follow-up. Staged hepatectomy after initial control of haemorrhage does not preclude a curative resection.