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Pediatric Nephrology

Issue 3/2018

Content (22 Articles)

Review

Adherence in pediatric kidney transplant recipients: solutions for the system

Elizabeth A. Steinberg, Mary Moss, Cindy L. Buchanan, Jens Goebel

Open Access Review

Continually improving standards of care: The UK Renal Registry as a translational public health tool

Lucy A. Plumb, Alexander J. Hamilton, Carol D. Inward, Yoav Ben-Shlomo, Fergus J. Caskey

Open Access Educational Review

Dysfunctional voiding: the importance of non-invasive urodynamics in diagnosis and treatment

Joanna C. Clothier, Anne J. Wright

Educational Review

Expanding the role of vasopressin antagonism in polycystic kidney diseases: From adults to children?

Peter Janssens, Caroline Weydert, Stephanie De Rechter, Karl Martin Wissing, Max Christoph Liebau, Djalila Mekahli

Clinical Quiz

Abdominal pain in a 5-year-old girl with bilateral nephromegaly: Questions

Hulya Nalcacioglu, Sibel Yel, Meriban Karadogan, Fatma Turkan Mutlu, Funda Bastug, Yasemin Altuner Torun

Clinical Quiz

Abdominal pain in a 5-year-old girl with bilateral nephromegaly: Answers

Hulya Nalcacioglu, Sibel Yel, Meriban Karadogan, Fatma Turkan Mutlu, Funda Bastug, Yasemin Altuner Torun

Clinical Quiz

An adolescent boy progressing insidiously to end-stage renal disease: Questions

Aysun Çaltık Yılmaz, Bahar Buyukkaragoz, Selcuk Kivilcim, Aslı Celebi Tayfur, Sacit Gunbey

Clinical Quiz

An adolescent boy progressing insidiously to end-stage renal disease: Answers

Aysun Çaltık Yılmaz, Bahar Buyukkaragoz, Selcuk Kivilcim, Aslı Celebi Tayfur, Sacit Gunbey

Original Article

Mutations in INF2 may be associated with renal histology other than focal segmental glomerulosclerosis

Anja K. Büscher, Nora Celebi, Peter F. Hoyer, Hanns-Georg Klein, Stefanie Weber, Julia Hoefele

Original Article

Diffuse mesangial sclerosis in a PDSS2 mutation-induced coenzyme Q10 deficiency

Béla Iványi, Gábor Z. Rácz, Péter Gál, Kitti Brinyiczki, István Bódi, Tibor Kalmár, Zoltán Maróti, Csaba Bereczki

Original Article

Effects of growth hormone treatment on adult height in severely short children with X-linked hypophosphatemic rickets

Nadine Meyerhoff, Dieter Haffner, Hagen Staude, Elke Wühl, Michaela Marx, Rolf Beetz, Uwe Querfeld, Martin Holder, Heiko Billing, Wolfgang Rabl, Carmen Schröder, Olaf Hiort, Jürgen H. Brämswig, Annette Richter-Unruh, Dirk Schnabel, Miroslav Živičnjak

Original Article

Complement functional tests for monitoring eculizumab treatment in patients with atypical hemolytic uremic syndrome: an update

Gianluigi Ardissino, Francesca Tel, Martina Sgarbanti, Donata Cresseri, Antenore Giussani, Samantha Griffini, Elena Grovetto, Ilaria Possenti, Michela Perrone, Sara Testa, Fabio Paglialonga, Piergiorgio Messa, Massimo Cugno

Original Article

Immunohistochemical and serological characterization of membranous nephropathy in children and adolescents

Anne K. Dettmar, Thorsten Wiech, Markus J. Kemper, Armin Soave, Michael Rink, Jun Oh, Rolf A. K. Stahl, Elion Hoxha

Original Article

Clinical and genetic heterogeneity in familial steroid-sensitive nephrotic syndrome

Guillaume Dorval, Olivier Gribouval, Vanesa Martinez-Barquero, Eduardo Machuca, Marie-Josèphe Tête, Véronique Baudouin, Stéphane Benoit, Imen Chabchoub, Gérard Champion, Dominique Chauveau, Hassib Chehade, Chokri Chouchane, Sylvie Cloarec, Pierre Cochat, Karin Dahan, Jacques Dantal, Yahsou Delmas, Georges Deschênes, Phillippe Dolhem, Dominique Durand, Zelal Ekinci, Khalil El Karoui, Michel Fischbach, Jean-Pierre Grunfeld, Vincent Guigonis, Mongia Hachicha, Julien Hogan, Maryvonne Hourmant, Aurélie Hummel, Nassim Kamar, Thierry Krummel, Didier Lacombe, Brigitte Llanas, Laurent Mesnard, Nabil Mohsin, Patrick Niaudet, Hubert Nivet, Paloma Parvex, Christine Pietrement, Loic de Pontual, Claire Pouteil Noble, David Ribes, Pierre Ronco, Eric Rondeau, Marion Sallee, Michel Tsimaratos, Tim Ulinski, Rémi Salomon, Corinne Antignac, Olivia Boyer

Original Article

Hyperammonemia associated with distal renal tubular acidosis or urinary tract infection: a systematic review

Caterina M. Clericetti, Gregorio P. Milani, Sebastiano A. G. Lava, Mario G. Bianchetti, Giacomo D. Simonetti, Olivier Giannini

Original Article

Prevalence and associated factors of renal dysfunction and proteinuria in cyanotic congenital heart disease

Nattaphorn Hongsawong, Prapimdaw Khamdee, Suchaya Silvilairat, Wattana Chartapisak

Original Article

Acute kidney injury in necrotizing enterocolitis predicts mortality

Cory N. Criss, David T. Selewski, Bipin Sunkara, Joshua S. Gish, Lily Hsieh, Jennifer S. Mcleod, Jason O. Robertson, Niki Matusko, Samir K. Gadepalli

Original Article

Fluid overload independent of acute kidney injury predicts poor outcomes in neonates following congenital heart surgery

Kenneth E. Mah, Shiying Hao, Scott M. Sutherland, David M. Kwiatkowski, David M. Axelrod, Christopher S. Almond, Catherine D. Krawczeski, Andrew Y. Shin

Original Article

Preoperative levels of urinary uromodulin predict acute kidney injury after pediatric cardiopulmonary bypass surgery

Michael R. Bennett, Olivia Pyles, Qing Ma, Prasad Devarajan