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Published in: The International Journal of Cardiovascular Imaging 5/2014

01-06-2014 | Images in Cardiology

Severe mitral stenosis as the first manifestation of systemic lupus erythematosus in a 20-year-old woman: the value of magnetic resonance imaging in the diagnosis of Libman-Sacks endocarditis

Authors: Hervé Gouya, Laure Cabanes, Luc Mouthon, Alain Pavie, Paul Legmann, Olivier Vignaux

Published in: The International Journal of Cardiovascular Imaging | Issue 5/2014

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Abstract

We report a case of severe mitral stenosis caused by Libman-Sacks endocarditis, as an initial manifestation of systemic lupus erythematosus (SLE) in a 20-year-old woman. Cardiac magnetic resonance imaging (MRI) demonstrated a thickening of the mitral valve with basal endocardial thickening exhibiting defect on first-pass perfusion short-axis acquisition and delayed enhancement in keeping with extensive fibrous endocarditis. The patient underwent successful mechanical mitral valve replacement. This case illustrates that MRI is useful in diagnosing this recognised but uncommon cardiac complication of SLE and excluding differential diagnosis such as valve tumour and infective endocarditis with perivalvular abscesses.
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Metadata
Title
Severe mitral stenosis as the first manifestation of systemic lupus erythematosus in a 20-year-old woman: the value of magnetic resonance imaging in the diagnosis of Libman-Sacks endocarditis
Authors
Hervé Gouya
Laure Cabanes
Luc Mouthon
Alain Pavie
Paul Legmann
Olivier Vignaux
Publication date
01-06-2014
Publisher
Springer Netherlands
Published in
The International Journal of Cardiovascular Imaging / Issue 5/2014
Print ISSN: 1569-5794
Electronic ISSN: 1875-8312
DOI
https://doi.org/10.1007/s10554-014-0418-8

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