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Child's Nervous System
Published in: Child's Nervous System 4/2008

01-04-2008 | Case Report

Serial changes in white matter lesions in a neonate with incontinentia pigmenti

Authors: J. H. Lee, S. A. Im, J. S. Chun

Published in: Child's Nervous System | Issue 4/2008

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Abstract

Case report

We report an infant who presented with clinical manifestations of incontinentia pigmenti (IP). Despite experiencing seizures in the early neonatal period, the patient had normal growth and development until recently. However, follow-up magnetic resonance imaging revealed sequential changes in white matter lesions.

Discussion

The pathogenesis of neurological involvement in IP has not been clearly elucidated and appears to be associated with various mechanisms, including developmental, destructive, and vascular processes. We have attempted to explain the pathogenesis of IP through these changes.
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Metadata
Title
Serial changes in white matter lesions in a neonate with incontinentia pigmenti
Authors
J. H. Lee
S. A. Im
J. S. Chun
Publication date
01-04-2008
Publisher
Springer-Verlag
Published in
Child's Nervous System / Issue 4/2008
Print ISSN: 0256-7040
Electronic ISSN: 1433-0350
DOI
https://doi.org/10.1007/s00381-007-0550-z

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