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01-03-2013 | Clinical Brief

Selective Arterial Embolization of Giant Renal Tuberous Sclerosis

Authors: Valentina De Pasquale, Gianluigi Natali, Piergiorgio Falappa, Simona Gerocarni Nappo, Annamaria Salerno, Paolo Caione

Published in: Indian Journal of Pediatrics | Issue 3/2013

Abstract

Different minimally invasive methods have been proposed to treat renal manifestation of tuberous sclerosis complex (TSC), in order to preserve kidney parenchyma and avoid nephrectomy. The case of a boy with bleeding giant angiomyolipoma treated by selective arterial embolization is discussed. The extensive renal lesions resulted significantly decreased, with resolution of arterial hypertension and abdominal symptoms. Differential renal function increased from 26.6% to 32.6%. Renal involvement in TSC requires careful parenchymal-sparing procedures. Selective embolization of the main renal lesions should be considered as first line therapy.

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Title: Selective Arterial Embolization of Giant Renal Tuberous Sclerosis
Authors: Valentina De Pasquale
Gianluigi Natali
Piergiorgio Falappa
Simona Gerocarni Nappo
Annamaria Salerno
Paolo Caione
Publication date: 01-03-2013
Publisher: Springer-Verlag
Published in: Indian Journal of Pediatrics / Issue 3/2013
Print ISSN: 0019-5456
Electronic ISSN: 0973-7693
DOI: https://doi.org/10.1007/s12098-012-0716-x

At a glance: The STEP trials

Springer Medicine

Selective Arterial Embolization of Giant Renal Tuberous Sclerosis

Abstract

At a glance: The STEP trials

Springer Medicine

Abstract

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