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General Thoracic and Cardiovascular Surgery

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01-03-2019 | Case Report

Removal of an endometrioid stromal sarcoma from the inferior vena cava and right atrium

Authors: Hesham Alkady, Sobhy Abouramadan, Mohamed Nagy, Ahmed Talaat, Tarek Hashem, Abdalla Khaleel

Published in: General Thoracic and Cardiovascular Surgery | Issue 3/2019

Abstract

Entometrioid stromal sarcomas are seen in extra-uterine as well as extra-gonadal sites and have a strong association with endometriosis. Although having better prognosis than other sarcomas, yet these tumors may relapse (whether local or distant) in up to 56% of cases, even as late as 20 years after surgery. We report a case of a 30-year-old female patient with a mass in the inferior vena cava and right atrium which was surgically removed using cardiopulmonary bypass and deep hypothermic circulatory arrest and turned to be an entometrioid stromal sarcoma. The patient gave a history of endometriosis followed by the appearance of a low-grade ovarian endometrioid stromal sarcoma 4 years before the development of the mass in the IVC and right atrium.

Diesing D, Cordes T, Finas D, Löning M, Mayer K, et al. Endometrial stromal sarcomas—a retrospective analysis of 11 patients. Anticancer Res. 2006;26:655–61.PubMed

Wong J, Tan G, Chia C, Selvarajan S, Teo M. A rare case of multiple malignancies arising in endometriosis: diffuse extra-uterine high-grade endometrial stromal sarcoma and ovarian carcinoma. Am J Cancer Case Rep. 2015;3:1–8.

Mourra N, Tiret E, Parc Y, de Saint-Maur P, Parc R, et al. Endometrial stromal sarcoma of the rectosigmoid colon arising in extragonadal endometriosis and revealed by portal vein thrombosis. Arch Pathol Lab Med. 2001;125:1088–90.PubMed

Alaaraj R, Lataifeh I, Elsaadi J, Salameh M, Sughayer M. Primary low-grade endometrioid stromal sarcoma of the ovary with multiple omental metastases. Gulf Med J. 2016;5:69–73.

Ali RH, Rouzbahman M. Endometrial stromal tumors revisited: an update based on the 2014 WHO classification. J Clin Pathol. 2015;68:325–32.CrossRefPubMed

Al-Ebrahim KE. Right atrial mass: the dilemma of diagnosis and when not to operate (letter). Ann Thorac Surg. 2009;87:2005.CrossRefPubMed

Lauten A, Strauch JT, Wippermann J, Wahlers T. A rare type of right atrial tumor in a 66-year-old woman. J Thorac Cardiovasc Surg. 2007;133:251–2.CrossRefPubMed

Chiappini B, Savini C, Marinelli G, Martin Suarez S, DiEusanio M, et al. Cavoatrial tumor thrombus: single-stage surgical approach with profound hypothermia and circulatory arrest, including a review of the literature. J Thorac Cardiovasc Surg. 2002;124:684–8.CrossRefPubMed

Title: Removal of an endometrioid stromal sarcoma from the inferior vena cava and right atrium
Authors: Hesham Alkady
Sobhy Abouramadan
Mohamed Nagy
Ahmed Talaat
Tarek Hashem
Abdalla Khaleel
Publication date: 01-03-2019
Publisher: Springer Singapore
Published in: General Thoracic and Cardiovascular Surgery / Issue 3/2019
Print ISSN: 1863-6705
Electronic ISSN: 1863-6713
DOI: https://doi.org/10.1007/s11748-018-0902-5

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Removal of an endometrioid stromal sarcoma from the inferior vena cava and right atrium

Abstract

Keynote webinar | Spotlight on medication adherence

Springer Medicine

Abstract

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