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Pediatric Nephrology

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01-10-2016 | Clinical Quiz

Refractory arterial hypertension and renal failure combined with cerebral seizures and pancytopenia in a 5-year-old girl with bilateral nephromegaly: Answers

Authors: Patrick Hundsdoerfer, Uwe Querfeld

Published in: Pediatric Nephrology | Issue 10/2016

Excerpt

No. Impairment of the bone marrow function is untypical for nephroblastomatosis.

Lymphoblastic lymphoma/acute lymphoblastic leukemia.

Fine needle biopsy of the kidney and bone marrow puncture.

Glucocorticoids followed by multi-drug chemotherapy.

…

Lin CC, Tsai JD, Lin SP, Lee HC (2005) Renal sonographic findings of type I glycogen storage disease in infancy and early childhood. Pediatr Radiol 35:786–791CrossRefPubMed

Alessandri JL, Cuillier F, Ramful D, Ernould S, Robin S, de Napoli-Cocci S, Riviere JP, Rossignol S (2008) Perlman syndrome: report, prenatal findings and review. Am J Med Genet A 146A:2532–2537CrossRefPubMed

Owens CM, Brisse HJ, Olsen OE, Begent J, Smets AM (2008) Bilateral disease and new trends in Wilms tumour. Pediatr Radiol 38:30–39CrossRefPubMed

Mussa A, Peruzzi L, Chiesa N, De Crescenzo A, Russo S, Melis D, Tarani L, Baldassarre G, Larizza L, Riccio A, Silengo M, Ferrero GB (2012) Nephrological findings and genotype-phenotype correlation in Beckwith-Wiedemann syndrome. Pediatr Nephrol 27:397–406CrossRefPubMed

Goldman M, Smith A, Shuman C, Caluseriu O, Wei C, Steele L, Ray P, Sadowski P, Squire J, Weksberg R, Rosenblum ND (2002) Renal abnormalities in Beckwith-Wiedemann syndrome are associated with 11p15.5 uniparental disomy. J Am Soc Nephrol 13:2077–2084CrossRefPubMed

Reiter A, Schrappe M, Ludwig WD, Tiemann M, Parwaresch R, Zimmermann M, Schirg E, Henze G, Schellong G, Gadner H, Riehm H (2000) Intensive ALL-type therapy without local radiotherapy provides a 90% event-free survival for children with T-cell lymphoblastic lymphoma: a BFM group report. Blood 95:416–421PubMed

Malbrain ML, Lambrecht GL, Daelemans R, Lins RL, Hermans P, Zachee P (1994) Acute renal failure due to bilateral lymphomatous infiltrates. Primary extranodal non-Hodgkin's lymphoma (p-EN-NHL) of the kidneys: does it really exist? Clin Nephrol 42:163–169PubMed

Tornroth T, Heiro M, Marcussen N, Franssila K (2003) Lymphomas diagnosed by percutaneous kidney biopsy. Am J Kidney Dis 42:960–971CrossRefPubMed

Dobkin SF, Brem AS, Caldamone AA (1991) Primary renal lymphoma. J Urol 146:1588–1590PubMed

10.

Neglia JP, Day DL, Swanson TV, Ramsay NK, Robison LL, Nesbit ME Jr (1988) Kidney size at diagnosis of childhood acute lymphocytic leukemia: lack of prognostic significance for outcome. Am J Pediatr Hematol Oncol 10:296–300CrossRefPubMed

11.

Attard-Montalto SP, Saha V, Ng YY, Kingston JE, Eden OB (1994) High incidence of hypertension in children presenting with acute lymphoblastic leukemia. Pediatr Hematol Oncol 11:519–525CrossRefPubMed

12.

Olgar S, Yetgin S, Cetin M, Aras T (2006) Can renal leukemic infiltration cause hypertension in children? J Pediatr Hematol Oncol 28:579–584CrossRefPubMed

Title: Refractory arterial hypertension and renal failure combined with cerebral seizures and pancytopenia in a 5-year-old girl with bilateral nephromegaly: Answers
Authors: Patrick Hundsdoerfer
Uwe Querfeld
Publication date: 01-10-2016
Publisher: Springer Berlin Heidelberg
Published in: Pediatric Nephrology / Issue 10/2016
Print ISSN: 0931-041X
Electronic ISSN: 1432-198X
DOI: https://doi.org/10.1007/s00467-015-3183-6

Keynote webinar | Spotlight on medication adherence

Springer Medicine

Refractory arterial hypertension and renal failure combined with cerebral seizures and pancytopenia in a 5-year-old girl with bilateral nephromegaly: Answers

Excerpt

Keynote webinar | Spotlight on medication adherence

Springer Medicine

Excerpt

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