Published in:
Open Access
01-12-2010 | Case report
Recurrent hemorrhagic pericardial effusion in a child due to diffuse lymphangiohemangiomatosis: a case report
Authors:
Shyam S Kothari, Sanjiv Sharma, Kinjal Bhatt, Ruma Ray, Sameer Bakhshi, Ujjwal Chowdhury
Published in:
Journal of Medical Case Reports
|
Issue 1/2010
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Abstract
Introduction
Recurrent hemorrhagic pericardial effusion in children with no identifiable cause is a rare presentation.
Case presentation
We report the case of a 4-year-old Indian girl who presented with recurrent hemorrhagic pericardial effusion. Diffuse lymphangiomatosis was suspected when associated pulmonary involvement, soft tissue mediastinal mass, and lytic bone lesions were found. Pericardiectomy and lung biopsy confirmed the diagnosis of diffuse lymphangiohemangiomatosis. Partial clinical improvement occurred with thalidomide and low-dose radiotherapy, but our patient died from progressive respiratory failure.
Conclusion
Diffuse lymphangiohemangiomatosis should be considered in the differential diagnosis of hemorrhagic pericardial effusion of unclear cause.