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Published in: Journal of Medical Case Reports 1/2010

Open Access 01-12-2010 | Case report

Recurrent hemorrhagic pericardial effusion in a child due to diffuse lymphangiohemangiomatosis: a case report

Authors: Shyam S Kothari, Sanjiv Sharma, Kinjal Bhatt, Ruma Ray, Sameer Bakhshi, Ujjwal Chowdhury

Published in: Journal of Medical Case Reports | Issue 1/2010

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Abstract

Introduction

Recurrent hemorrhagic pericardial effusion in children with no identifiable cause is a rare presentation.

Case presentation

We report the case of a 4-year-old Indian girl who presented with recurrent hemorrhagic pericardial effusion. Diffuse lymphangiomatosis was suspected when associated pulmonary involvement, soft tissue mediastinal mass, and lytic bone lesions were found. Pericardiectomy and lung biopsy confirmed the diagnosis of diffuse lymphangiohemangiomatosis. Partial clinical improvement occurred with thalidomide and low-dose radiotherapy, but our patient died from progressive respiratory failure.

Conclusion

Diffuse lymphangiohemangiomatosis should be considered in the differential diagnosis of hemorrhagic pericardial effusion of unclear cause.
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Metadata
Title
Recurrent hemorrhagic pericardial effusion in a child due to diffuse lymphangiohemangiomatosis: a case report
Authors
Shyam S Kothari
Sanjiv Sharma
Kinjal Bhatt
Ruma Ray
Sameer Bakhshi
Ujjwal Chowdhury
Publication date
01-12-2010
Publisher
BioMed Central
Published in
Journal of Medical Case Reports / Issue 1/2010
Electronic ISSN: 1752-1947
DOI
https://doi.org/10.1186/1752-1947-4-62

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