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01-09-2010 | Case Report

Pulmonary interstitial glycogenosis in the setting of lung growth abnormality: radiographic and pathologic correlation

Authors: Monette Castillo, Aruna Vade, Jennifer Eden Lim-Dunham, Emi Masuda, Rasan Massarani-Wafai

Published in: Pediatric Radiology | Issue 9/2010

Abstract

Pulmonary interstitial glycogenosis (PIG) is a rare pediatric interstitial lung disease. We report a case of a term boy presenting with tachypnea at birth requiring supplemental oxygen. Chest radiographs followed by high-resolution CT (HRCT) demonstrated hyperinflation and diffuse interstitial markings interspersed with multiple cystic spaces. An open lung biopsy demonstrated a minor component of PIG superimposed upon poor alveolarization. PIG in the setting of lung growth abnormality might be more common than previously described. Additionally, radiographic findings associated with most pediatric interstitial lung diseases are nonspecific, and histopathologic correlation is essential for diagnosis.

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Title: Pulmonary interstitial glycogenosis in the setting of lung growth abnormality: radiographic and pathologic correlation
Authors: Monette Castillo
Aruna Vade
Jennifer Eden Lim-Dunham
Emi Masuda
Rasan Massarani-Wafai
Publication date: 01-09-2010
Publisher: Springer-Verlag
Published in: Pediatric Radiology / Issue 9/2010
Print ISSN: 0301-0449
Electronic ISSN: 1432-1998
DOI: https://doi.org/10.1007/s00247-010-1670-2

At a glance: The STEP trials

Springer Medicine

Pulmonary interstitial glycogenosis in the setting of lung growth abnormality: radiographic and pathologic correlation

Abstract

At a glance: The STEP trials

Springer Medicine

Abstract

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