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Clinical Sarcoma Research
Published in: Clinical Sarcoma Research 1/2020

01-12-2020 | Propranolol | Case Report

A case report of Kaposiform haemangioendothelioma; response with propranolol and steroids

Authors: Saurav Verma, Ekta Dhamija, Adarsh Barwad, Venkatesan S. Kumar, Sameer Rastogi

Published in: Clinical Sarcoma Research | Issue 1/2020

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Abstract

Background

Kaposiform haemangioendothelioma is a rare vascular tumor and may involve skin, deep soft tissue or bone. It is a locally aggressive tumor usually seen in infants. Here we report a case of kaposiform hemagioendothelioma in a child who responded to propranolol and steroids.

Case presentation

A 3-year-old male child presented with a swelling below his right knee with characteristic violet skin lesion. There was no evidence of Kasabach–Merritt phenomenon. After no improvement with several attempts at debridement and anti-tubercular treatment; a diagnosis of Kaposiform Haemangioendothelioma was reached on the basis of overall clinical picture and histology. The child was treated with propranolol and steroids and had an excellent clinical response and a near complete resolution on imaging at 5 months.

Conclusions

These cases are often misdiagnosed and despite a delay in diagnosis have good outcomes with appropriate multimodality management. This case highlights the unique and typical characteristics of kaposiform haemangioendothelioma.
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Metadata
Title
A case report of Kaposiform haemangioendothelioma; response with propranolol and steroids
Authors
Saurav Verma
Ekta Dhamija
Adarsh Barwad
Venkatesan S. Kumar
Sameer Rastogi
Publication date
01-12-2020
Publisher
BioMed Central
Keyword
Propranolol
Published in
Clinical Sarcoma Research / Issue 1/2020
Electronic ISSN: 2045-3329
DOI
https://doi.org/10.1186/s13569-020-00134-8

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