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Published in: Journal of Medical Case Reports 1/2011

Open Access 01-12-2011 | Case report

Primitive neuroectodermal tumor of the cervix: a case report

Authors: Farah Farzaneh, Hamidreza Rezvani, Parisa Taherzadeh Boroujeni, Farzaneh Rahimi

Published in: Journal of Medical Case Reports | Issue 1/2011

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Abstract

Introduction

Peripheral primitive neuroectodermal tumor of the cervix uteri is extremely rare. Between 1987 and 2010, there were only nine cases reported in the English literature, with considerably different management policies.

Case presentation

A 45-year-old Iranian woman presented to our facility with a primitive neuroectodermal tumor of the cervix uteri. Her clinical stage IB2 tumor was treated successfully with chemotherapy. Our patient underwent radical hysterectomy. There was no trace of the tumor after four years of follow-up.

Conclusions

According to current knowledge, primitive neuroectodermal tumors belong to the Ewing's sarcoma family, and the improvement of treatment outcome in our patient was due to dose-intensive neoadjuvant chemotherapy, surgery and consolidation chemotherapy in accordance with the protocol for bony Ewing's sarcoma.
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Metadata
Title
Primitive neuroectodermal tumor of the cervix: a case report
Authors
Farah Farzaneh
Hamidreza Rezvani
Parisa Taherzadeh Boroujeni
Farzaneh Rahimi
Publication date
01-12-2011
Publisher
BioMed Central
Published in
Journal of Medical Case Reports / Issue 1/2011
Electronic ISSN: 1752-1947
DOI
https://doi.org/10.1186/1752-1947-5-489

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