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01-05-2013 | Case Report

Primary Pancreatic Ewing's Sarcoma with Portal Vein Tumor Thrombosis

Authors: Chris Reilly, Scott Zenoni, Muhammad K. Hasan, Shyam Varadarajulu, Tien-Anh Tran, Sebastian G. de la Fuente, Juan P. Arnoletti

Published in: Journal of Gastrointestinal Surgery | Issue 5/2013

Abstract

Background

Extraosseous Ewing's sarcoma (EES) is a mesenchyme-derived small blue cell tumor, which is distinguished by its rarity, aggressiveness, dismal prognosis, and distinct pathogenesis. Occurring almost exclusively among children and young adults, EES can arise from a variety of organs and portends a rapid clinical deterioration and high likelihood of recurrence.

Discussion

We present the first reported case of a primary pancreatic Ewing's sarcoma in a patient with concomitant portal vein thrombosis. The atypical presentation of this extraordinarily rare tumor underscores the imperative to maintain EES in the differential diagnosis of suspicious, indistinct pancreatic lesions in young patients. In addition, we review the available literature describing additional cases of primary pancreatic Ewing's sarcoma.

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Title: Primary Pancreatic Ewing's Sarcoma with Portal Vein Tumor Thrombosis
Authors: Chris Reilly
Scott Zenoni
Muhammad K. Hasan
Shyam Varadarajulu
Tien-Anh Tran
Sebastian G. de la Fuente
Juan P. Arnoletti
Publication date: 01-05-2013
Publisher: Springer-Verlag
Published in: Journal of Gastrointestinal Surgery / Issue 5/2013
Print ISSN: 1091-255X
Electronic ISSN: 1873-4626
DOI: https://doi.org/10.1007/s11605-012-2098-9

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Springer Medicine

Primary Pancreatic Ewing's Sarcoma with Portal Vein Tumor Thrombosis

Abstract

Background

Discussion

At a glance: The ONWARDS insulin icodec trials

Springer Medicine

Abstract

Background

Discussion

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