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Journal of Children's Orthopaedics

Published in:

01-03-2007 | Original Clinical Article

Pre-axial mirror polydactyly associated with tibial deficiency: a study of the patterns of skeletal anomalies of the foot and leg

Authors: Renjit Verghese, Hitesh Shah, Gleeson Rebello, Benjamin Joseph

Published in: Journal of Children's Orthopaedics | Issue 1/2007

Abstract

Purpose

The study was undertaken to identify the patterns and spectrum of aberrant development of the skeletal elements of the leg and foot in children with pre-axial mirror polydactyly of the foot.

Methods

Case records and radiographs of eight children (ten feet) with pre-axial mirror polydactyly were studied. Four feet were seen in association with fibular dimelia, three feet with dysplastic trapezoid shaped tibia, two with tibial aplasia and one with tibial hypoplasia.

Results

Distinct patterns of anomalies of the hindfoot, midfoot and forefoot were noted, with different patterns of leg malformation. Fibular dimelia was associated with duplication of the calcaneum, cuboid and the lateral cuneiform. Talar duplication occurred in children with a trapezoidal tibia. No duplication of tarsal bones was seen in association with tibial aplasia or hypoplasia. The first metatarsal was hypoplastic wherever the tibia failed to develop. Mere resection of the supernumerary rays resulted in a near normal looking foot in feet without calcaneal duplication. The cosmetic appearance of the foot was poorest in children with fibular dimelia.

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Title: Pre-axial mirror polydactyly associated with tibial deficiency: a study of the patterns of skeletal anomalies of the foot and leg
Authors: Renjit Verghese
Hitesh Shah
Gleeson Rebello
Benjamin Joseph
Publication date: 01-03-2007
Publisher: Springer Berlin Heidelberg
Published in: Journal of Children's Orthopaedics / Issue 1/2007
Print ISSN: 1863-2521
Electronic ISSN: 1863-2548
DOI: https://doi.org/10.1007/s11832-006-0001-5

At a glance: The STEP trials

Springer Medicine

Pre-axial mirror polydactyly associated with tibial deficiency: a study of the patterns of skeletal anomalies of the foot and leg

Abstract

Purpose

Methods

Results

At a glance: The STEP trials

Springer Medicine

Abstract

Purpose

Methods

Results

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